1Department of Urology, Peking University First Hospital, Institute of
Urology, Peking University, National Urological Cancer Center, Beijing
100034, China; 2Department of General Surgery, Peking University
First Hospital, Beijing 100034, China
A 26-year-old man with abdominal distention and fever for
6 months was found to have a huge cystic mass in the right
retroperitoneal space, which was confirmed by Computer
Tomography(CT) and had close relationship with right kidney.
A radical resection of the tumor was performed and Wilms'
tumor was confirmed by pathological assay.
A 26-year-old man with continuous abdominal distention
and fever for more than 6 months, and the maximum body
temperature was 38.8 centigrade degree. The patient had
the history of renal calculi for 4 years, and sclerosing agent
injection treatment for renal cyst 5 years ago. A high tension cystic tumor could be palpated in the right upper region of
abdomen. Computer Tomography showed a lesion located in
the retroperitoneal space, and had close relationship with kidney
and psoas muscle. It was misdiagnosed to be recurrent renal cyst
and hydronephrosis initially in other institutes, so the patient
received ureteral stent insertion of right ureter and percutaneous
puncture and drainage of the cystic mass, which were not
effective. The patient underwent a surgical procedure. During the
operation, it was found that a partial cystic and partial solid mass
derived from right kidney, which almost took over all room of
the right retroperitoneal space. The tumor was removed radically,
and the final pathological evaluation showed a Wilms' tumor.
Wilms' tumor is one of the most common malignant solid tumor
of infant, most being diagnosed in the first 5 years of the life, but
it is extremely rare in adults. In adults, it has a poorer prognosis
than in children even for the same stage. Currently, most studies
recommend combining treatment of operation, chemotherapy
and radiotherapy. But due to the rarity of the lesion, a standard
treatment for this disease has not been well established.